A CASE OF IDIOPATHIC SCLEREDEMA: A RARE ENTITY

*Meenakshi Garg, Shweta Kumari, Dharmendra Kumar Mishra and Raj Kishor

ABSTRACT

Scleredema is a fibromucinous connective tissue disease characterized by symmetric, nonpitting edema and induration of the face, neck and trunk. Although the pathogenesis remains elusive, associations with infection, diabetes mellitus, and paraproteinemia have been established. We report here a case of scleredema in a 40 years old male patient with progressive thickening and induration of the skin over upper arms, face, anterior and posterior trunk since 6 months. On histopathology, markedly thickened reticular dermis with thickened collagen bundles and abundant mucin in between was found. We are reporting this case in view of its rarity and lack of effective treatment modalities.

Keywords: Scleredema, non pitting, diabetes mellitus, paraproteinemia.