A RARE CASE REPORT OF NEUROFIBROMATOSIS TYPE 1 IN HARD PALATE REGION

*Dr. Sayan Mandal, Dr. Subhransu Basu, Dr. Rajarshi Banerjee and Dr. Debraj Samanta

ABSTRACT

Neurofibroma is a benign peripheral nerve sheath tumor comprising variable mixture of Schwann cells, perineurial-like cells, and fibroblasts. Neurofibroma may occur as solitary lesion or as part of a generalised syndrome of neurofibromatosis or very rarely as multiple neurofibromas without any associated syndrome. Here, we present a case of a 42-year-old male patient with NF-1. Patient have generalized freckling and café au lait spots throughout the body since 10-12 years and a diffused swelling measuring about 3 cm × 2 cm, extending from the right maxillary hard palate region to the midpalate since 1year. The diagnosis of NF-1 was made according to the presence of two or more diagnostic criteria of the National Institute of Health Consensus Development Conference. No recurrence was observed in a 6-month follow-up after extensive surgical ablation.

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