INFLAMMATORY LINEAR VERRUCOUS EPIDERMAL NEVUS IN THE PERIANAL AND VULVAL REGION: A CASE REPORT AND SHORT REVIEW OF THE LITERATURE.

*Dr. Richa Patel, Dr. Yasmeen Khatib, Dr. Meena Makhija, Dr. Nitin Chikhale

ABSTRACT

Inflammatory linear verrucous epidermal nevus (ILVEN) is a unilateral, persistent, linear, pruritic eruptions that usually appear on an extremity in infancy or childhood. These lesions are resistant to therapy. It is commonly found over buttocks and lower limbs. ILVEN in perineum and vulva is very rare. ILVEN may be an isolated finding or may be associated with other abnormalities. The diagnosis may sometimes be difficult and necessitate biopsy and advanced immunohistochemical analysis. The management usually is only symptomatic and often unsatisfactory. ILVEN occasionally presents in the inguinogenital region and in this area may, like many vulval naevi, be misdiagnosed as vulvitis, psoriasis, genital warts or sexual abuse. We present a case of ILVEN in a 26-year-old female in perivulval and perianal region and provide a short review of the literature, with emphasis on our current understanding of the etiology, clinical presentation, histopathological features and differentials along with its management.

Keywords: Inflammatory linear verrucous epidermal nevus, pruritic eruptions, perineum, perianal, vulva.