RECURRENT GIANT FIBROSARCOMA ARISING IN DERMATOFIBROSARCOMA PROTUBERANS WITH DISTANT LUNG METASTASIS

*Ozinko M.O., Otei, O.O., Ekpo R.G., Asuquo M., Ofutet E.O

ABSTRACT

Dermatofibrosarcoma protuberans (DFSP) is a rare skin tumor which typically arises in the dermis as a multi-nodular mass, and then spreads into the subcutaneous tissues and muscles but rarely metastasize. Only few cases of gluteal dermatofibrosarcoma protuberans have been reported to metastasize to the lungs. This is a histologically proven case of fibrosarcoma arising from DFSP of the gluteal area with deep muscle extension and distant metastasis to the lungs, evaluated with chest x-ray and abdominal ultrasound. Treatment is by surgery, radiotherapy and immunotherapy.

Keywords: Dermatofibrosarcoma protuberans, lung metastasis, muscle extension, immunotherapy