A CASE OF MADRAS PATTERN OF MOTOR NEURON DISEASE - CASE REPORT

Salabha Ann Mathew*, Vishnu V. K., Nina Joseph, Kazia Sunny, S. Haja Sherief and T. Sivakumar

ABSTRACT

A case of Madras pattern of Motor Neuron Disease (MMND) is a unique geographically distribution preponderantly reported from Southern part of India that is presented and other forms of Motor Neuron Disease are discussed. This disease affect males and females in an equal rate. Disease condition happened to have wasting confined to distal part of limbs known to be Lower Motor Neuron (LMD)disease and Upper Motor Neuron (UMD) together pyramidal dysfunction. We present a18 years old female presented with atrophy and weakness of left and right legs and is unable to walk for about 3 years who is early diagnosed with MMND. There is no wasting of proximal and trunk muscles and also have normal tone regardless of the presence of extensor plantar response, deep tendon reflexes are elicited. The involved group of muscles have power about 4/5.The patient also had multiple lower cranial nerve palsies and sensorineural hearing loss. With supportive treatment, the patient feels better. Continuing physiotherapy, regular monitoring of sensory and motor system with the disease condition makes a profound effect of patients healthy life.

Keywords: Madras Motor Neuron Disease, Lower Motor Neuron Disease, Upper Motor Neuron Disease.