CASE SERIES OF PRIMARY AMENORRHEA DUE TO MULLERIAN AGENESIS ENCOUNTERED IN BSMMU HOSPITAL

*Dr. Berkheez Shabir and Dr. Zahoor Hussain Daraz

ABSTRACT

Congenital anomalies of the female reproductive tract may involve the cervix, uterus, fallopian tubes or vagina. Woman’s obstetric and gynecologic health may be inimically affected, depending upon the type of congenital defect. In this case series patients presenting in the outpatient department of BSMMU hospital with Primary amenorrhea due to Mullerian agenesis were studied. Mullerian agenesis is found to occur in 1 out of every 4,000–10,000 females.[1] Patients with Mullerian agenesis commonly present with congenital absence of the vagina, uterus, or both, which also is referred to as Mullerian aplasia, Mayer–Rokitansky–Küster–Hauser syndrome or vaginal agenesis. In BSMMU these patients were offered optimium management and were followed up. Satisfactory vaginal creation was nonsurgically managed with successive vaginal dilation and surgically by neovagina creation. After one year of study period it was clear that most of these patients with few exceptions were treated optimally and they could live a healthy and better life.

Keywords: Mullerian agenesis, Primary amenorrhea, BSMMU (Bangabandhu Sheikh Mujib Medical University).