KAWASAKI DISEASE: CASE OF 12 YEARS OLD MALE PAEDIATRIC PATIENT WITH RARE MULTISYSTEM INFLAMMATORY DISEASE

Dr. Zahra Fadaeian* and Dr. Manoochehr Fadaeian

ABSTRACT

Kawasaki disease is an acute multisystem inflammatory disease of blood vessels This disease will commonly affects infants and young children. The disease may be characterized by a high fever, inflammation of the mucous membranes of the mouth and throat, a reddish skin rash, and lymphadenopathy. In most children may experience symptoms such as irritability, diarrhea, vomiting, coughing, arthritis, pain and swelling. Other associated abnormalities may include hepatosplenomegaly, aseptic meningitis, otitis media. However, in many cases around 50% the child will experience heart involvement inflammation of arteries that transport blood to heart muscle (coronary arteritis), associated bulging of the walls may develop myocarditis, which is associated with a tachycardia, decreased lower heart chamber functioning , heart involvement may include pericarditis , aortic or mitral valve insufficiency due to the linkage. In severe cases impaired ability of the heart to effectively pump blood to the lungs and the rest of the body. This damages can leads to heart failure. This complication is inflammation of arteries that provide oxygen-rich blood to heart muscle (coronary arteritis) and possible weakening, widening (dilation), and bulging (aneurysms) of affected arterial walls. Dilation and aneurysm formation occur in approximately 3 to 20 %of patients. In severe cases, complications may include the development of blood clots in the ballooned area with obstruction of blood flow, bursting (rupture) of an aneurysm.

Keywords: Kawasaki disease, (Cardiac) MRI, Coronary aneurysm, Cardiac imaging , (IVIG) , coronary artery lesion.